ICD-11 classes
08 Diseases of the nervous system
Epilepsy or seizures
8A61 — Genetic or presumed genetic syndromes primarily expressed...
8A61.1 — Genetic epileptic syndromes with onset in infancy
8A61.11 — Dravet syndrome

ICD-11 8A61.11 — Dravet syndrome

A refractory epileptic encephalopathy occurring in otherwise healthy infants during the first year of life with clonic/tonic-clonic, generalised and unilateral seizures, hemiclonic or generalised status epilepticus. The interictal EEG may initially be normal but with time background activity deteriorates and bilateral asymmetric, focal or multifocal paroxysms of polyspike and slow-waves appear. Mutations in the voltage-gated sodium channel gene SCN1A are commonly found.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.