ICD-11 classes
08 Diseases of the nervous system
Diseases of neuromuscular junction or muscle
Myasthenia gravis or certain specified neuromuscular...
8C62 — Lambert-Eaton syndrome
ICD-11 8C62 — Lambert-Eaton syndrome
Lambert-Eaton myasthenic syndrome, 20 times as rare as Acetylcholine receptor positive Myasthenia gravis with a prevalence of 3.42 per million, is an immune-mediated disease of the neuromuscular junction. Clinically the disease is characterised by proximal weakness of the legs. In most patients, the weakness extends to other muscles including the oculobulbar ones. Autonomic symptoms (dry mouth, erectile dysfunction, constipation) are frequent. Tendon reflexes are reduced. Repetitive nerve stimulation shows low Compound muscle action potentials, decrement >10% al low frequency and increment >100% after maximum voluntary contraction at high frequency.
The diagnosis includes nothing.
The diagnosis excludes nothing.
It has no clarifying diagnoses.
The diagnosis is coded elsewhere: