ICD-11 classes
08 Diseases of the nervous system
Diseases of neuromuscular junction or muscle
Primary disorders of muscles
8C70 — Muscular dystrophy

ICD-11 8C70 — Muscular dystrophy

Progressive, hereditary skeletal muscle diseases characterised by muscle weakness, wasting, defects in muscle proteins, necrosis of muscle tissue and replacement of muscle tissue with connective and fatty tissue.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 8C70 contains 10 clarifying diagnoses:

  1. 8C70.0 — Becker muscular dystrophy
  2. 8C70.1 — Duchenne muscular dystrophy
  3. 8C70.2 — Emery-Dreifuss muscular dystrophy
  4. 8C70.3 — Facioscapulohumeral muscular dystrophy
  5. 8C70.4 — Limb-girdle muscular dystrophy
    It contains 4 clarifying diagnoses.
  6. 8C70.5 — Scapuloperoneal muscular dystrophy
  7. 8C70.6 — Congenital muscular dystrophy
  8. 9C82.1 — Muscular dystrophy affecting extraocular muscle
  9. 8C70.Y — Other specified muscular dystrophy
  10. 8C70.Z — Muscular dystrophy, unspecified

The diagnosis is coded elsewhere:

The diagnosis is included in 3 other classes.

  • Muscular dystrophy affecting extraocular muscle (9C82.1)
  • Barth syndrome (5C50.E0)
  • Epidermolysis bullosa simplex with muscular dystrophy (EC30)

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