ICD-11 classes
08 Diseases of the nervous system
Diseases of neuromuscular junction or muscle
Primary disorders of muscles
8C76 — Myofibrillar myopathy
ICD-11 8C76 — Myofibrillar myopathy
Myofibrillar myopathies are a heterogeneous group of disorders, characterised by the pathologic finding of myofibrillar disruption on electron microscope with a spectrum of histological abnormalities including excessive desmin accumulation in muscle fibres.
The diagnosis includes nothing.
It excludes 2 items.
- Myasthenia gravis or certain specified neuromuscular junction disorders (8C60-8C6Z)
- Secondary myopathies (8C80-8C8Z)
It has no clarifying diagnoses.
The diagnosis is coded elsewhere:
- Primary disorders of muscles #10017