ICD-11 classes
08 Diseases of the nervous system
Diseases of neuromuscular junction or muscle
Primary disorders of muscles
4A41 — Idiopathic inflammatory myopathy
4A41.0 — Dermatomyositis
4A41.01 — Juvenile dermatomyositis

ICD-11 4A41.01 — Juvenile dermatomyositis

Juvenile dermatomyositis is the early-onset form of dermatomyositis, a systemic autoimmune inflammatory muscle disorder, characterised by proximal muscle weakness, evocative skin lesion, and systemic manifestations.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Dermatomyositis #3632
• Dermatomyositis #10074
• Dermatomyositis #15830
• Dermatomyositis #17257
• Dermatomyositis #18360