ICD-11 classes
08 Diseases of the nervous system
Human prion diseases
8E01 — Acquired prion disease
8E01.2 — Variant Creutzfeldt-Jakob Disease

ICD-11 8E01.2 — Variant Creutzfeldt-Jakob Disease

A disease of the brain, that is suspected to be caused by a prion associated with Bovine Spongiform Encephalopathy. This disease is characterised by a long incubation period, psychiatric symptoms followed by neurological deficits, and is fatal. Transmission may be by ingestion of food (with a bovine origin) contaminated with infected brain or spinal cord from an infected cow, or blood transfusion. Confirmation is by pathological examination of the brain.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Acquired prion disease #1436