ICD-11 classes
08 Diseases of the nervous system
Other disorders of the nervous system
8E41 — Pachymeningitis
8E41.1 — Idiopathic hypertrophic pachymeningitis

ICD-11 8E41.1 — Idiopathic hypertrophic pachymeningitis

Inflammation of the pachymeninges resulting in localised or diffuse thickening of the dura mater for which no identifiable cause is found. The cranial and/or the spinal dura may be affected. Neurological features includes headache, visual disturbance, cranial nerve palsies, ataxia and with spinal involvement, limb weakness, sensory impairment and sphincter disturbances . Diagnosis may be aided by neuroimaging and spinal fluid analysis and dural biopsy.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Pachymeningitis #676
• Pachymeningitis #8797