ICD-11 classes
09 Diseases of the visual system
Strabismus or ocular motility disorders
Diseases of neuromuscular junction or muscle
Primary disorders of muscles
8C70 — Muscular dystrophy
8C70.4 — Limb-girdle muscular dystrophy

ICD-11 8C70.4 — Limb-girdle muscular dystrophy

Limb-girdle muscular dystrophy (LGMD) constitutes a group of genetically determined, progressive disorders of muscles, in which the pelvic or shoulder girdle musculature is predominantly or primarily involved. It may be inherited in an autosomal recessive or dominant fashion.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 8C70.4 contains 4 clarifying diagnoses:

  1. 8C70.40 — Dominant limb-girdle muscular dystrophy
  2. 8C70.41 — Recessive limb-girdle muscular dystrophy
  3. 8C70.4Y — Other specified limb-girdle muscular dystrophy
  4. 8C70.4Z — Limb-girdle muscular dystrophy, unspecified

The diagnosis is coded elsewhere:

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