ICD-11 classes
09 Diseases of the visual system
Strabismus or ocular motility disorders
Diseases of neuromuscular junction or muscle
Primary disorders of muscles
4A41 — Idiopathic inflammatory myopathy
4A41.2 — Inclusion body myopathy
4A41.21 — Noninflammatory inclusion body myopathy

ICD-11 4A41.21 — Noninflammatory inclusion body myopathy

Noninflammatory inclusion body myopathy (IBM) is an idiopathic muscle disorder without inflammatory exudates and expression of class I major histocompatibility complex. Rimmed vacuoles and “IBM-like” filaments without inflammatory cells are described in muscle biopsy.

The diagnosis includes nothing.

It excludes 1 item.

  • Myasthenia gravis or certain specified neuromuscular junction disorders (8C60-8C6Z)

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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