ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of cutaneous blood and lymphatic vessels
EF40 — Vasculitis or capillaritis involving the skin
EF40.1 — Vasculitis affecting small cutaneous blood vessels
EF40.10 — Urticarial vasculitis
4A44.91 — Hypocomplementaemic urticarial vasculitis

ICD-11 4A44.91 — Hypocomplementaemic urticarial vasculitis

Vasculitis accompanied by urticaria and hypocomplementemia affecting small vessels (i.e., capillaries, venules, or arterioles), and associated with anti-C1q antibodies. Glomerulonephritis, arthritis, obstructive pulmonary disease, and ocular inflammation are common.(Chapel Hill Consensus Conference, 2011)

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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