ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of cutaneous blood and lymphatic vessels
EF40 — Vasculitis or capillaritis involving the skin
EF40.1 — Vasculitis affecting small cutaneous blood vessels
4A44.A — Antineutrophil cytoplasmic antibody-associated vasculitis
4A44.A0 — Microscopic polyangiitis

ICD-11 4A44.A0 — Microscopic polyangiitis

Necrotizing vasculitis, with few or no immune deposits, predominantly affecting small vessels (i.e., capillaries, venules, or arterioles). Necrotizing arteritis involving small and medium sized arteries may be present. Necrotizing glomerulonephritis is very common. Pulmonary capillaritis often occurs. Granulomatous inflammation is absent.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Antineutrophil cytoplasmic antibody-associated vasculitis #3686
• Antineutrophil cytoplasmic antibody-associated vasculitis #18414