ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of cutaneous blood and lymphatic vessels
EF40 — Vasculitis or capillaritis involving the skin
EF40.1 — Vasculitis affecting small cutaneous blood vessels
4A44.A — Antineutrophil cytoplasmic antibody-associated vasculitis
4A44.A1 — Granulomatosis with polyangiitis

ICD-11 4A44.A1 — Granulomatosis with polyangiitis

Necrotizing granulomatous inflammation usually involving the upper and lower respiratory tract, and necrotizing vasculitis affecting predominantly small to medium-sized vessels (e.g., capillaries, venules, arterioles, arteries and veins). Necrotizing glomerulonephritis is common . (Arthritis Rheum 1990; 33:1101-1107)

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

• Antineutrophil cytoplasmic antibody-associated vasculitis #3686
• Antineutrophil cytoplasmic antibody-associated vasculitis #18414