ICD-11 classes
14 Diseases of the skin
Skin disorders involving specific cutaneous structures
Disorders of cutaneous blood and lymphatic vessels
EF40 — Vasculitis or capillaritis involving the skin
EF40.1 — Vasculitis affecting small cutaneous blood vessels
4A44.A — Antineutrophil cytoplasmic antibody-associated vasculitis
4A44.A2 — Eosinophilic granulomatosis with polyangiitis

ICD-11 4A44.A2 — Eosinophilic granulomatosis with polyangiitis

Eosinophil-rich and necrotizing granulomatous inflammation often involving the respiratory tract, and necrotizing vasculitis predominantly affecting small to medium-sized vessels, and associated with asthma and eosinophilia. ANCA is most frequent when glomerulonephritis is present. (Arthritis Rheum 1990; 33:1094-1100)

It includes 1 item.

  • Churg-Strauss syndrome

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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