ICD-11 classes
03 Diseases of the blood or blood-forming organs
Coagulation defects, purpura or other haemorrhagic or...
Coagulation defects
Congenital or constitutional haemorrhagic condition

ICD-11 Congenital or constitutional haemorrhagic condition

A condition caused by determinants arising during the antenatal period or genetically inherited factors, leading to defects in clotting mechanisms or abnormalities causing structural flaws in the blood vessels. This disease is characterised by spontaneous bleeding or bruising.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis contains 8 clarifying diagnoses:

  1. 3B10 — Hereditary factor VIII deficiency
    It contains 4 clarifying diagnoses.
  2. 3B11 — Hereditary factor IX deficiency
    It contains 3 clarifying diagnoses.
  3. 3B12 — Von Willebrand disease
  4. 3B13 — Haemophilia C
  5. 3B14 — Other inherited coagulation factor deficiency with bleeding tendency
    It contains 4 clarifying diagnoses.
  6. 3B15 — Inherited coagulation factor deficiency without bleeding tendency
  7. Congenital non-inherited haemorrhagic condition
    It contains 1 clarifying diagnosis.
  8. 3B1Z — Congenital or constitutional haemorrhagic condition, unspecified

The diagnosis is included in 1 another class.

  • Congenital non-inherited haemorrhagic condition

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