ICD-11 classes
03 Diseases of the blood or blood-forming organs
Coagulation defects, purpura or other haemorrhagic or...
Coagulation defects
Congenital or constitutional haemorrhagic condition
3B10 — Hereditary factor VIII deficiency

ICD-11 3B10 — Hereditary factor VIII deficiency

A disease caused by a genetically inherited mutation leading to a deficiency in clotting due to lack of factor VIII. This disease is characterised by increasing haemorrhaging and bruising. Confirmation is by identification of mutations by genetic testing.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 3B10 contains 4 clarifying diagnoses:

  1. 3B10.0 — Haemophilia A
  2. 3B10.1 — Hereditary factor VIII deficiency with anti-factor VIII inhibitor
  3. 3B10.Y — Other specified hereditary factor VIII deficiency
  4. 3B10.Z — Hereditary factor VIII deficiency, unspecified

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