ICD-11 classes
03 Diseases of the blood or blood-forming organs
Coagulation defects, purpura or other haemorrhagic or...
Coagulation defects
Congenital or constitutional haemorrhagic condition
3B10 — Hereditary factor VIII deficiency
3B10.0 — Haemophilia A
ICD-11 3B10.0 — Haemophilia A
Haemophilia A is the most common form of haemophilia characterised by spontaneous or prolonged haemorrhages due to factor VIII deficiency. Depending on the extent of the factor VIII deficiency, it can be severe (biological activity of factor VIII below 1%), moderately severe (activity of factor VIII between 1% and 5%), or mild (activity of factor VIII between 5 and 40%).
It includes 4 items.
- Severe haemophilia A
- Moderately severe haemophilia A
- Mild haemophilia A
- Symptomatic form of haemophilia A in female carriers
It excludes 1 item.
- factor VIII deficiency with vascular defect (3B12)
It has no clarifying diagnoses.