ICD-11 classes
03 Diseases of the blood or blood-forming organs
Coagulation defects, purpura or other haemorrhagic or...
Coagulation defects
Congenital or constitutional haemorrhagic condition
3B14 — Other inherited coagulation factor deficiency with bleeding...

ICD-11 3B14 — Other inherited coagulation factor deficiency with bleeding tendency

Any disease caused by genetically inherited mutations leading to lack of coagulation factors in the blood not elsewhere classified. These diseases are characterised by increased haemorrhaging and bruising as the blood cannot clot properly to control bleeding. Confirmation is identification of mutations by genetic testing.

The diagnosis includes nothing.

The diagnosis excludes nothing.

Diagnosis with code 3B14 contains 4 clarifying diagnoses:

1. 3B14.0 — Hereditary deficiency of factor I
2. 3B14.1 — Hereditary factor X deficiency
3. 3B14.2 — Combined deficiency of vitamin K-dependent clotting factors
4. 3B14.Z — Other inherited coagulation factor deficiency with bleeding tendency, unspecified