ICD-11 classes
03 Diseases of the blood or blood-forming organs
Coagulation defects, purpura or other haemorrhagic or...
Coagulation defects
Congenital or constitutional haemorrhagic condition
3B14 — Other inherited coagulation factor deficiency with bleeding...
3B14.2 — Combined deficiency of vitamin K-dependent clotting factors

ICD-11 3B14.2 — Combined deficiency of vitamin K-dependent clotting factors

Hereditary combined vitamin K-dependent clotting factors deficiency (VKCFD) is a congenital bleeding disorder resulting from variably decreased levels of coagulation factors II, VII, IX and X, as well as natural anticoagulants protein C, protein S and protein Z.

The diagnosis includes nothing.

The diagnosis excludes nothing.

It has no clarifying diagnoses.

The diagnosis is coded elsewhere:

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